ACAD8 Antibody

Catalog Number:

36014

Amount:

100μg

Price:

$319

Swiss-Prot No:

Swiss-Prot#: Q9UKU7
NCBI Gene ID: 27034
Gene Accssion: BC001964

Form of Antibody:

Rabbit IgG in pH7.4 PBS, 0.05% NaN3, 40% Glycerol.

Storage/Stability:

Immunogen:

Fusion protein corresponding to residues near the C terminal of human acyl-CoA dehydrogenase family, member 8

Purification:

Antigen affinity purification.

Specificity/Sensitivity:

The antibody detects endogenous levels of total ACAD8 protein.

Applications:

IHC

Background:

This gene encodes a member of the acyl-CoA dehydrogenase family of enzymes that catalyze the dehydrogenation of acyl-CoA derivatives in the metabolism of fatty acids or branch chained amino acids. The encoded protein is a mitochondrial enzyme that functions in catabolism of the branched-chain amino acid valine. Defects in this gene are the cause of isobutyryl-CoA dehydrogenase deficiency.

References:

appl_detail:

Immunohistochemistry: 1:15-1:50

Datasheet PDF