BCS1L antibody

Catalog Number:

31919

Amount:

100μg

Price:

$319

Swiss-Prot No:

Swiss-Prot#: Q96QA5
NCBI Protein#: BC000416

Form of Antibody:

pH7.4 PBS, 0.05% NaN3, 40% Glycerol

Storage/Stability:

Immunogen:

Fusion protein of human BCS1L

Purification:

Antigen affinity purification

Specificity/Sensitivity:

Applications:

IHC

Background:

This gene encodes a homolog of the S. cerevisiae bcs1 protein which is involved in the assembly of complex III of the mitochondrial respiratory chain. The encoded protein does not contain a mitochondrial targeting sequence but experimental studies confirm that it is imported into mitochondria. Mutations in this gene are associated with mitochondrial complex III deficiency and the GRACILE syndrome. Several alternatively spliced transcripts encoding two different isoforms have been described.

References:

appl_detail:

IHC dilution:1:50-1:300

Datasheet PDF