PCCA Polyclonal Antibody

Catalog Number:

31714

Amount:

100μg

Price:

$319

Swiss-Prot No:

Swiss-Prot#:P05165
NCBI Gene ID:5095

Form of Antibody:

Avoid freeze / thaw cycles.|Buffer: PBS with 50% glycerol, pH7.4.

Storage/Stability:

Immunogen:

Recombinant fusion protein of human PCCA (NP_000273.2).

Purification:

Affinity purification

Specificity/Sensitivity:

Applications:

WB

Background:

The protein encoded by this gene is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA encodes the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia. Multiple transcript variants encoding different isoforms have been found for this gene.

References:

appl_detail:

WB 1:1000 - 1:3000

Datasheet PDF